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lipoyl-4-aminobenzoic acid
biotinidase substrate
Also Known As:
L-PABA; lipo-PAB; lipoyl-p-aminobenzoate
Networked:
1
relevant articles (
0
outcomes,
0
trials/studies)
Bio-Agent Context: Research Results
Organic Chemicals: 133
Hydrocarbons: 1713
Cyclic Hydrocarbons: 97
Aromatic Hydrocarbons: 291
Benzene Derivatives: 17
Benzoates: 426
Aminobenzoates: 1
para-Aminobenzoates: 43
lipoyl-4-aminobenzoic acid: 1
Carboxylic Acids: 973
Thioctic Acid: 2074
lipoyl-4-aminobenzoic acid: 1
Carbocyclic Acids
Benzoates: 426
Aminobenzoates: 1
para-Aminobenzoates: 43
lipoyl-4-aminobenzoic acid: 1
Sulfur Compounds: 278
Thiophenes: 257
Thioctic Acid: 2074
lipoyl-4-aminobenzoic acid: 1
Enzymes and Coenzymes: 1
Coenzymes: 558
Thioctic Acid: 2074
lipoyl-4-aminobenzoic acid: 1
Lipids: 114793
Fatty Acids: 27405
Thioctic Acid: 2074
lipoyl-4-aminobenzoic acid: 1
Related Diseases
1.
Biotinidase Deficiency (Multiple Carboxylase Deficiency, Late Onset)
08/31/1990 - "
In addition, children with profound biotinidase deficiency (less than 10% normal serum activity) have greatly reduced levels of L-pABA hydrolyzing activity in serum (less than 15% of mean normal activity) and obligate heterozygotes have activities intermediate between that of normal and profoundly deficient individuals.
"