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dihydrolipoamide acyltransferase

component of branched-chain 2-oxo acid dehydrogenase multienzyme complex; mutation in this (E2) catalytic subunit identifies type II maple syrup urine disease; do not confuse with E2 enzymes of pyruvate dehydrogenase (PDC) and alpha-ketoglutarate dehydrogenase complexes
Also Known As:
BCOADC-E2; E2 transacylase; branched chain acyltransferase; dihydrolipoyl transacylase
Networked: 18 relevant articles (0 outcomes, 0 trials/studies)

Bio-Agent Context: Research Results

Experts

1. Bryk, Ruslana: 1 article (03/2008)
2. Cao, Hua: 1 article (03/2008)
3. Cherian, Joseph: 1 article (03/2008)
4. Converse, Paul J: 1 article (03/2008)
5. Ehrt, Sabine: 1 article (03/2008)
6. Gold, Benjamin: 1 article (03/2008)
7. Gurney, Mark: 1 article (03/2008)
8. Hotha, Srinivas: 1 article (03/2008)
9. Jiang, Xiuju: 1 article (03/2008)
10. Lin, Gang: 1 article (03/2008)

Related Diseases

1. Biliary Liver Cirrhosis (Primary Biliary Cirrhosis)
2. Maple Syrup Urine Disease
3. Chronic Hepatitis C
4. Autoimmune Hepatitis
5. Tuberculosis (Tuberculoses)

Related Drugs and Biologics

1. dihydrolipoamide succinyltransferase
2. Enzymes
3. Autoantigens
4. Autoantibodies
5. 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) (Alpha-Keto Acid Dehydrogenase)
6. Antigens
7. Mitochondrial Proteins (Mitochondrial Protein)
8. Complementary DNA (cDNA)
9. Thiamine (Aneurin)
10. Messenger RNA (mRNA)