lactosylceramide beta-galactosidase

Networked: 3 relevant articles (0 outcomes, 0 trials/studies)

1.	Globoid Cell Leukodystrophy (Krabbe Disease) 07/01/1975 - "The lactosylceramide beta-galactosidase activity was only moderately reduced in leukocytes, but strongly reduced in cerebral tissue from patients with Krabbe's disease. " 03/25/1975 - "With our own assay system, hepatic lactosylceramide beta-galactosidase appeared deficient only in Gm1-gangliosidosis, while it appeared deficient only in globoid cell leukodystrophy when the assay system of Wenger et al. (Wenger, D.A., Sattler, M., Clark, D., and McKelvey, H. " 03/25/1975 - "In view of recent conflicting reports from two laboratories, activities of lactosylceramide beta-galactosidase were reinvestigated in detail in brains and livers of normal individuals and of patients with globoid cell leukodystrophy or GM1-gangliosidosis. " 12/17/1975 - "Tissues from patients with Krabbe's disease were found to be deficient in lactosylceramide beta-galactosidase activity (lactosylceramidase I) when pure taurocholate was used in the assay. "
2.	GM1 Gangliosidosis (Gangliosidosis GM1) 12/17/1975 - "In place of crude taurocholate the pure salts of glycodeoxycholate, taurodeoxycholate and taurochenodeoxycholate worked even better to stimulate the second lactosylceramide beta-galactosidase activity and GM1 gangliosidosis patients exhibiting little if any activity. "
3.	Sphingolipidoses (Sphingolipidosis) 03/25/1975 - "Lactosylceramide beta-galactosidase in human sphingolipidoses. "

1.	Taurodeoxycholic Acid
2.	Taurocholic Acid (Sodium Taurocholate)
3.	Taurochenodeoxycholic Acid
4.	Salts
5.	Glycodeoxycholic Acid
6.	lactosylceramidase