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beta-ureidopropionase
Also Known As:
N-carbamoyl beta-alanine amidohydrolase; beta-alanine synthase; N-carbamoyl-beta-alanine amidohydrolase
Networked:
2
relevant articles (
0
outcomes,
0
trials/studies)
Bio-Agent Context: Research Results
Enzymes and Coenzymes: 1
Enzymes: 152586
Hydrolases: 2166
Amidohydrolases: 43
beta-ureidopropionase: 2
Experts
1.
Kuhara, Tomiko
: 1 article (12/2002)
Related Diseases
1.
Hyperammonemia
12/05/2002 - "
In this review, the differential diagnosis for hyperammonemia are described; deficiencies of ornithine carbamoyl transferase, argininosuccinate synthase (citrullinemia), argininosuccinate lyase and arginase, lysinuric protein intolerance, hyperammonemia-hyperornithinemia-homocitrullinemia syndrome, and citrullinemia type II. The diagnosis of IEM of purine and pyrimidine such as deficiencies of hypoxanthine-guanine phosphoribosyl transferase, adenine phosphoribosyl transferase, dihydropyrimidine dehydrogenase, dihydropyrimidinase and beta-ureidopropionase are described.
"
2.
Citrullinemia
12/05/2002 - "
In this review, the differential diagnosis for hyperammonemia are described; deficiencies of ornithine carbamoyl transferase, argininosuccinate synthase (citrullinemia), argininosuccinate lyase and arginase, lysinuric protein intolerance, hyperammonemia-hyperornithinemia-homocitrullinemia syndrome, and citrullinemia type II. The diagnosis of IEM of purine and pyrimidine such as deficiencies of hypoxanthine-guanine phosphoribosyl transferase, adenine phosphoribosyl transferase, dihydropyrimidine dehydrogenase, dihydropyrimidinase and beta-ureidopropionase are described.
"
3.
Protein Deficiency
10/01/1991 - "
Protein deficiency (5%) also decreased the activity of beta-ureidopropionase.
"
4.
Lysinuric Protein Intolerance
12/05/2002 - "
In this review, the differential diagnosis for hyperammonemia are described; deficiencies of ornithine carbamoyl transferase, argininosuccinate synthase (citrullinemia), argininosuccinate lyase and arginase, lysinuric protein intolerance, hyperammonemia-hyperornithinemia-homocitrullinemia syndrome, and citrullinemia type II. The diagnosis of IEM of purine and pyrimidine such as deficiencies of hypoxanthine-guanine phosphoribosyl transferase, adenine phosphoribosyl transferase, dihydropyrimidine dehydrogenase, dihydropyrimidinase and beta-ureidopropionase are described.
"
Related Drugs and Biologics
1.
Dihydrouracil Dehydrogenase (NADP) (Dihydropyrimidine Dehydrogenase)
2.
Carboxyl and Carbamoyl Transferases (Carbamoyltransferases)
3.
Hypoxanthine
4.
Transferases
5.
Ornithine
6.
Guanine
7.
Argininosuccinate Synthase (Argininosuccinate Synthetase)
8.
Argininosuccinate Lyase
9.
Arginase
10.
Adenine