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Isolated Noncompaction of the Ventricular Myocardium Summary

Description: Rare congenital cardiomyopathies characterized by the lack of left ventricular myocardium compaction. The noncompaction results in numerous prominent trabeculations and a loose myocardial meshwork (spongy myocardium) in the LEFT VENTRICLE. Heterogeneous clinical features include diminished systolic function sometimes associated with left ventricular dilation, that presents either neonatally or progressively. Often, the RIGHT VENTRICLE is also affected. CONGESTIVE HEART FAILURE; PULMONARY EMBOLISM; and ventricular ARRHYTHMIA are commonly seen.

Also Known As: Isolated Non-compaction of the Ventricular Myocardium; Isolated Noncompaction of the Left Ventricular Myocardium, X-Linked; Noncompaction of the Left Ventricular Myocardium, Autosomal Dominant

Networked: 7 relevant articles (0 outcomes, 0 trials/studies) for this Disease

Key Drugs and Agents for Isolated Noncompaction of the Ventricular Myocardium

Efficacy Chart >>
Drugs and Important Biological Agents (IBA) related to treatments:
  1. Brain Natriuretic Peptide (Natrecor) : 1 result : FDA 1
  2. Gadolinium : 1 result : IBA

Diseases Related to Isolated Noncompaction of the Ventricular Myocardium

  1. Ventricular Tachycardia
  2. Cardiac Sudden Death (Sudden Cardiac Arrest)
  3. Ventricular Fibrillation
  4. Muscular Diseases (Myopathy)
  5. Long QT Syndrome
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Key Therapies for Isolated Noncompaction of the Ventricular Myocardium

Efficacy Chart >>
  1. Defibrillators (Defibrillator) : 3 results
  2. Cardiac Resynchronization Therapy : 1 result
  3. Implantable Defibrillators (Implantable Cardioverter-Defibrillator) : 1 result

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