We describe two neonates with anatomically corrected malposition of the great arteries (ACM). A 1-day-old female newborn, who had the salient clinical findings of
Goldenhar syndrome, behaved like a patient with the
tetralogy of Fallot. The cardiac malformations included ACM, perimembranous inlet and outlet
ventricular septal defect with tricuspid valve straddling, conoventricular septal malaligement, bilateral cori without aortic-mitral continuity,
pulmonary stenosis at subvalvular, valvular, and supravalvular levels, and bicuspid semilunar valves. After the procedure of left
Blalock-Taussig shunt at 3 months of age,
cyanosis was alleviated. The other 1-month-old male newborn, who presented with prolonged feeding,
tachypnea and
tachycardia, likened to a patient with the
hypoplastic left heart syndrome. He had a combination of ACM,
mitral stenosis, hypoplastic left atrium and left ventricle, a restrictive
patent foramen ovale,
ventricular septal defect, subaortic conus without aortic-mitral continuity, subaortic
stenosis, and a narrow ascending aortic root. Rashkind balloon atrioseptostomy was done with limited success. He survived a
Norwood procedure. Transarterial entry of the
catheter, which was inverted with the aid of balloon floating maneuver, to hook the retro-aortic pulmonary artery in ACM is recommended.