Successful heart transplantation in a patient with Ivemark syndrome combined with situs inversus, single atrium and ventricle after total cavo-pulmonary connection.

Abstract

Heart transplantation represents a valuable therapeutical option for patients with congenital heart disease and end-stage heart failure. We report the case of a young adult patient with a situs inversus and additional complex congenital malformations of the heart who underwent several prior palliative interventions, a biventricular repair being impossible. Orthotopic cardiac transplantation with several technical modifications was performed successfully at the age of 19 years.

• Authors: P A Berdat, P Mohacsi, U Althaus, T Carrel
• Journal: European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery (Eur J Cardiothorac Surg) Vol. 14 Issue 6 Pg. 631-4 (Dec 1998) ISSN: 1010-7940 [Print] Germany
• PMID: 9879878 (Publication Type: Case Reports, Journal Article)

Topics

• Abnormalities, Multiple (surgery)
• Adult
• Heart Bypass, Right
• Heart Defects, Congenital (complications, surgery)
• Heart Transplantation
• Humans
• Palliative Care (methods)
• Situs Inversus (complications)