| Abstract | A case of surgical repair of progressive exophthalmos of the right eye in a 43-year-old woman with neurofibromatosis Type 1 (NF1) is presented. Preoperatively, the patient's ocular movements and visual fields were intact. Visual acuity was 20/30 on the right side and 20/20 on the left. Computerized tomography scanning demonstrated complete absence of the superolateral orbital wall on the right side with a large meningocele protruding into the right orbit. Intraoperatively, a new superolateral wall was constructed using the inner table of the left frontal bone as a bone transplant. A free galeoperiosteum flap was used for water-tight dural reconstruction. A few weeks postoperatively the patient's exophthalmos showed remarkable resolution. Her ocular movements, visual acuity, and visual fields remained unchanged. In conclusion, reconstruction of the superolateral wall and repair of a meningocele in a patient with NF1 is worthwhile and can be followed by excellent cosmetic results. More important, the patient's visual functions remain preserved. |
| Authors | J de Vries, H P Freihofer, T Menovsky, J R Cruysberg
(Affiliation: Department of Neurosurgery, University of Nijmegen, The Netherlands.)
|
| Journal | Journal of neurosurgery
(J Neurosurg)
Vol. 89
Issue 6
Pg. 1032-5
(Dec 1998)
ISSN: 0022-3085 UNITED STATES |
| PMID | 9833833
(Publication Type: Case Reports, Journal Article)
|
| Topics |
- Adult
- Exophthalmos
(etiology, surgery)
- Female
- Humans
- Meningocele
(complications, radiography)
- Neurofibromatosis 1
(complications)
- Tomography, X-Ray Computed
- Treatment Outcome
|
