[Congenital bilateral perisylvian syndrome].

Abstract

The congenital bilateral perisylvian syndrome is characterized by pseudobulbar palsy, moderate delay in mental and motor development and epilepsy. Three characteristic case stories are presented. Epileptic seizures are most frequently generalized: tonic, astatic, atypical absences and tonic-clonic seizures. Partial seizures are less frequent. Seizure control is often unsatisfactory. Neuroimaging demonstrates thickening of the cerebral cortex in the perisylvian area bilaterally; these changes together with the clinical picture establish the diagnosis. The etiology is unknown.

• Authors: P M Olsen, P V Uldall, J Alving, H Pedersen
• Journal: Ugeskrift for laeger (Ugeskr Laeger) Vol. 160 Issue 29 Pg. 4307-9 (Jul 13 1998) ISSN: 0041-5782 [Print] Denmark
• Vernacular Title: Kongenit bilateralt perisylvant syndrom.
• PMID: 9679434 (Publication Type: Case Reports, English Abstract, Journal Article)

Topics

• Abnormalities, Multiple (diagnosis, physiopathology)
• Adolescent
• Bulbar Palsy, Progressive (congenital, diagnosis, physiopathology)
• Cerebral Cortex (abnormalities, pathology)
• Child
• Epilepsy (diagnosis, physiopathology)
• Female
• Humans
• Intellectual Disability (diagnosis, physiopathology)
• Male
• Psychomotor Disorders (diagnosis, physiopathology)
• Retrospective Studies
• Syndrome