[A case of asplenia in a sickle cell homozygote SS patient].

Abstract

One case of total splenic atrophy is reported in a patient with SS homozygous sickle-cell disease presenting no related malformation, thus recalling the IVEMARK syndrome. An abdominal echography and computed tomography are indispensable in order to confirm the absence of the anatomic spleen; this makes for a better follow-up of sickle-cell disease.

• Authors: K P N'Zi, K N'Dri, D N Ouattara, T Kone, A S Diabate, G C Gbazi, A T Djedje
• Journal: Bulletin de la Societe de pathologie exotique (1990) (Bull Soc Pathol Exot) Vol. 91 Issue 2 Pg. 156-7 ( 1998) ISSN: 0037-9085 [Print] France
• Vernacular Title: Un cas d'asplénie chez un drépanocytaire homozygote SS.
• PMID: 9642472 (Publication Type: Case Reports, Journal Article)

Topics

• Adolescent
• Anemia, Sickle Cell (diagnostic imaging, genetics, pathology)
• Homozygote
• Humans
• Spleen (abnormalities)
• Tomography, X-Ray Computed
• Ultrasonography