Abstract |
|
Authors | A J Lloyd, R G Gray, A Green |
Journal | Journal of inherited metabolic disease
(J Inherit Metab Dis)
Vol. 18
Issue 1
Pg. 48-55
( 1995)
ISSN: 0141-8955 [Print] United States |
PMID | 7623442
(Publication Type: Journal Article)
|
Chemical References |
- Serum Albumin
- Sulfhydryl Compounds
- Tyrosine
- Hydrolases
- beta-N-Acetylhexosaminidases
- fumarylacetoacetase
- Glutathione Synthase
- Glutathione
|
Topics |
- Amino Acid Metabolism, Inborn Errors
(blood)
- Fibroblasts
- Glutathione
(metabolism)
- Glutathione Synthase
(deficiency, metabolism)
- Humans
- Hydrolases
(deficiency)
- Liver
(cytology, enzymology, metabolism)
- Oxidation-Reduction
- Reference Values
- Serum Albumin
(metabolism)
- Sulfhydryl Compounds
(metabolism)
- Tyrosine
(blood)
- beta-N-Acetylhexosaminidases
(metabolism)
|