[Acquired angioneurotic edema caused by acquired deficiency of C1 esterase inhibitor disclosing lymphoproliferative syndrome. Apropos of a case, review of the literature].

Abstract

One case of acquired angio-neurotic oedema is described and discussed with the other cases recorded in literature since Caldwell's one in 1972. This entity is characterized by: --the late onset of angio-oedema but its presence only in about half cases, --a complement deficiency resulting from the lack of C1-esterase inhibitor, --the absence of familial identical cases, --the great frequency of associated illnesses overall lympho-proliferative diseases, --the therapeutic response to either etiologic treatment of the associated disease or to the symptomatic effect of drugs used in hereditary angio-neurotic oedema.

• Authors: J Chevrant-Breton, D Mazéas, M Bagot, M Henry, J Goasguen, J P Robin
• Journal: Annales de dermatologie et de venereologie (Ann Dermatol Venereol) Vol. 109 Issue 12 Pg. 1049-56 ( 1982) ISSN: 0151-9638 [Print] France
• Vernacular Title: Oedème angio-neurotique (acquis) par déficit acquis en inhibiteur de Ci-estérase révélateur d'un syndrome lympho-prolifératif. A propos d'un cas, revue de la littérature.
• PMID: 7171202 (Publication Type: Case Reports, English Abstract, Journal Article)

Chemical References

• Complement C1 Inactivator Proteins

Topics

• Aged
• Angioedema (etiology, immunology, therapy)
• Complement C1 Inactivator Proteins (blood, deficiency)
• Humans
• Lymphoproliferative Disorders (complications, immunology, therapy)
• Male
• Time Factors