Abstract |
A case of an adult polysaccharide myopathy is reported in a patient with progressive muscular atrophy and weakness of limb girdles. Histochemistry and electron microscopy showed in some muscle fibers, a storage material composed of amylopectin-like filaments. Biochemical results were normal and no enzyme deficiency was found. This case is compared with three other published cases. Pathological conditions with amylopectin or amylopectin-like storage material are reviewed.
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Authors | J F Pellissier, T de Barsy, J Bille, G Serratrice, M Toga |
Journal | Acta neuropathologica. Supplementum
(Acta Neuropathol Suppl)
Vol. 7
Pg. 292-6
( 1981)
ISSN: 0065-1435 [Print] Germany |
PMID | 6939255
(Publication Type: Case Reports, Journal Article)
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Chemical References |
- Polysaccharides
- Glycogen
- Amylopectin
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Topics |
- Amylopectin
(metabolism)
- Glycogen
(metabolism)
- Humans
- Male
- Microscopy, Electron
- Middle Aged
- Muscles
(enzymology, pathology)
- Muscular Atrophy
(enzymology, pathology)
- Polysaccharides
(metabolism)
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