Abstract |
|
Authors | J A DelValle, B Merinero, A Jiménez, M J García, M Ugarte, F Omeñaca, G Neustadt, J Quero |
Journal | Journal of inherited metabolic disease
(J Inherit Metab Dis)
Vol. 5
Issue 2
Pg. 121-4
( 1982)
ISSN: 0141-8955 [Print] United States |
PMID | 6820422
(Publication Type: Journal Article, Research Support, Non-U.S. Gov't)
|
Chemical References |
- 3-methylcitrate
- Amino Acids
- Citrates
- Hydroxybutyrates
- Lactates
- Pentanoic Acids
- Propionates
- 2-methyl-3-oxovaleric acid
- Lactic Acid
- 2-methyl-3-hydroxybutyric acid
- hydracrylic acid
- Carboxy-Lyases
- Methylmalonyl-CoA Decarboxylase
- 3-Hydroxybutyric Acid
|
Topics |
- 3-Hydroxybutyric Acid
- Amino Acid Metabolism, Inborn Errors
(diet therapy, metabolism)
- Amino Acids
(metabolism)
- Carboxy-Lyases
(deficiency)
- Citrates
(urine)
- Female
- Fibroblasts
(enzymology)
- Food, Formulated
- Humans
- Hydroxybutyrates
(urine)
- Infant, Newborn
- Lactates
(urine)
- Lactic Acid
(analogs & derivatives)
- Methylmalonyl-CoA Decarboxylase
- Pentanoic Acids
(urine)
- Propionates
(blood, urine)
|