Abstract |
|
Authors | K Bartlett, H Ng, J V Leonard |
Journal | Clinica chimica acta; international journal of clinical chemistry
(Clin Chim Acta)
Vol. 100
Issue 2
Pg. 183-6
(Jan 15 1980)
ISSN: 0009-8981 [Print] Netherlands |
PMID | 6766095
(Publication Type: Case Reports, Journal Article)
|
Chemical References |
- Acyl Coenzyme A
- Butyrates
- Crotonates
- Hydroxy Acids
- Propionates
- Valerates
- Carbon Dioxide
- beta-methylcrotonylglycine
- beta-hydroxyisovaleric acid
- Biotin
- Carboxy-Lyases
- Ligases
- Glycine
|
Topics |
- Acidosis
(urine)
- Acyl Coenzyme A
- Amino Acid Metabolism, Inborn Errors
(drug therapy, enzymology, urine)
- Biotin
(pharmacology, therapeutic use)
- Butyrates
(urine)
- Carbon Dioxide
- Carboxy-Lyases
(deficiency)
- Child, Preschool
- Crotonates
(urine)
- Female
- Fibroblasts
(enzymology)
- Glycine
(analogs & derivatives, urine)
- Humans
- Hydroxy Acids
(urine)
- Ligases
(deficiency)
- Mitochondria
(enzymology)
- Propionates
- Pyruvate Carboxylase Deficiency Disease
- Valerates
(urine)
|