Budd-Chiari syndrome. Historical and clinical review with an analysis of surgical corrective procedures.

Abstract

Seventeen patients who fulfilled the criteria for the Budd-Chiari syndrome (centrilobular congestion and necrosis, a defined postsinusoidal block, and rapid onset of ascites) have been analyzed in terms of cause, prognosis, and treatment. Causal factors included caval web or tumor, hepatic tumor, a hypocoagulable state, myeloproliferative disease, and veno-occlusive disease. Location of the outflow block was suprahepatic (vena cava or major hepatic veins) in 13 patients and intrahepatic in 4. In five patients, a side-to-side portacaval shunt was effective in dissipating ascites with restoration to a normal lifestyle, as were transatrial fracture of a caval web (one patient) and resection of a huge cystadenoma of the liver (one patient). A peritoneal shunt provided effective palliation in three patients.

• Authors: W V McDermott, M D Stone, A Bothe Jr, C Trey
• Journal: American journal of surgery (Am J Surg) Vol. 147 Issue 4 Pg. 463-7 (Apr 1984) ISSN: 0002-9610 [Print] United States
• PMID: 6324603 (Publication Type: Journal Article)

Topics

• Budd-Chiari Syndrome (diagnostic imaging, etiology, surgery)
• Carcinoma, Hepatocellular (complications)
• Cystadenoma (complications)
• Humans
• Leiomyosarcoma (complications)
• Liver Neoplasms (complications)
• Portacaval Shunt, Surgical
• Prognosis
• Radiography
• Venae Cavae (diagnostic imaging, surgery)