Bilateral papillary cystadenoma of the epididymis as a component of von Hippel-Lindau's syndrome: report of a case presenting as infertility.

Abstract

We report a case of bilateral papillary cystadenoma of the epididymis thought to be a component of the von Hippel-Lindau syndrome. The patient was hospitalized initially because of infertility. He had undergone a craniotomy 2 years previously for the diagnosis of a cerebellar hemangioblastoma. Funduscopy had revealed angiomatous lesions of the left eye. The von Hippel-Lindau syndrome is discussed briefly and the importance of long-term urological followup for possible presentation of silent renal carcinoma is emphasized. Patients with bilateral epididymal papillary cystadenoma are prone to have other components of the von Hippel-Lindau syndrome, and clinical studies are indicated in all such patients.

• Authors: J de Souza Andrade, E A Bambirra, O J Bicalho, A F de Souza
• Journal: The Journal of urology (J Urol) Vol. 133 Issue 2 Pg. 288-9 (Feb 1985) ISSN: 0022-5347 [Print] United States
• PMID: 3968752 (Publication Type: Case Reports, Journal Article)

Topics

• Adult
• Angiomatosis (complications)
• Cystadenoma (complications, pathology)
• Epididymis
• Humans
• Infertility, Male (etiology)
• Male
• Testicular Neoplasms (complications, pathology)
• von Hippel-Lindau Disease (complications, pathology)