[Malignant pheochromocytoma associated with Recklinghausen's disease. Apropos of a case. Value of new methods in the diagnosis of pheochromocytoma].

Abstract

After having reported the case of a pheochromocytoma associated to Recklinghausen's disease, the authors define the best criteria of detection and localization of the pheochromocytoma and study its association to phacomatoses. Headaches, bouts of tachycardia and excessive inappropriate diuresis are the most evocative clinical signs of a pheochromocytoma. The different hormones and their urinary metabolites must be titrated separately and repeatedly. Two other examinations, scanner and scintigraphy with MIBG, visualize quite reliably the tumor foci. Calcium inhibitors are quite effective in sudden blood pressure rises. The association described here, may be explained by the fact that the two pathologies belong to the group of neurocristopathies.

• Authors: E Tison, X Marchand, S Kacet, C Proye, J Lekieffre
• Journal: Annales de cardiologie et d'angeiologie (Ann Cardiol Angeiol (Paris)) Vol. 35 Issue 9 Pg. 551-5 (Nov 1986) ISSN: 0003-3928 [Print] France
• Vernacular Title: Phéochromocytome malin associé à une maladie de Recklinghausen. A propos d'un cas. Intérêt des nouvelles méthodes de diagnostic du phéochromocytome.
• PMID: 3101574 (Publication Type: Case Reports, English Abstract, Journal Article)

Topics

• Adrenal Gland Neoplasms (complications, diagnosis)
• Adult
• Humans
• Male
• Methods
• Neurofibromatosis 1 (complications)
• Pheochromocytoma (complications, diagnosis)