Abstract | INTRODUCTION: PATIENTS AND METHODS: We performed a descriptive retrospective study by identifying all patients that received a diagnosis of pulmonary atresia with intact ventricular septum and critical pulmonary stenosis between January 1996 and January 2018. We collected and analysed data regarding right ventricular morphology, surgical management, percutaneous intervention and medium- and long-term outcomes. RESULTS: 51 patients were admitted. A total of 9 patients (17.6%) died during the followup. None of the deceased patients had coronary artery to right ventricle fistulae. The median length of follow up in the 42 survivors was 8.9 years (1-16). The functional class based on the latest revision of the New York Heart Association classification was 1.2 for the overall sample. Survivors of critical pulmonary stenosis had a functional class of 1.1, and survivors of pulmonary atresia with intact ventricular septum a functional class of 1.6. There were no differences based on the presence or absence of coronary artery to right ventricle fistulae. CONCLUSIONS:
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Authors | Maria Vall Camell, Javier Rodríguez-Fanjul, Carles Bautista Rodríguez, Freddy Hermogenes Pradda, Jose María Caffarena-Calvar, Martín Iriondo Sanz, Joan Sánchez-de-Toledo |
Journal | Anales de pediatria
(An Pediatr (Engl Ed))
Vol. 91
Issue 5
Pg. 336-343
(Nov 2019)
ISSN: 2341-2879 [Electronic] Spain |
Vernacular Title | Manejo percutáneo de la atresia pulmonar con tabique interventricular íntegro y la estenosis pulmonar crítica. |
PMID | 30952598
(Publication Type: Journal Article)
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Copyright | Copyright © 2018. Publicado por Elsevier España, S.L.U. |
Topics |
- Female
- Follow-Up Studies
- Heart Defects, Congenital
(surgery)
- Humans
- Infant, Newborn
- Male
- Percutaneous Coronary Intervention
(methods)
- Pulmonary Atresia
(surgery)
- Pulmonary Valve Stenosis
(surgery)
- Retrospective Studies
- Treatment Outcome
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