[Pigmented dermatofibrosarcoma protuberans (Bednar's tumor)].

Abstract

Pigmented dermatofibrosarcoma protuberans, first described by Bednar under the term storiform neurofibroma, is an infrequent neoplasm accounting for 1 to 5% of cases of dermatofibrosarcoma protuberans. Bednar's tumor is composed of spindle shaped cells arranged in a distinctive storiform or carthwheel pattern, and melanin-containing dendritic cells scattered within the tumor. The differential diagnosis with (non-pigmented) dermatofibrosarcoma protuberans is based on the presence of this population of pigmented cells. Two cases of pigmented dermatofibrosarcoma protuberans (Bednar's tumor) are reported here in, and a discussion follows on the clinicopathological features of this neoplasm and the different hypotheses on its histogenesis.

• Authors: L Puig, J M De Moragas, X Matías-Guiu, A Moreno
• Journal: Medicina cutanea ibero-latino-americana (Med Cutan Ibero Lat Am) Vol. 16 Issue 4 Pg. 314-8 ( 1988) ISSN: 0210-5187 [Print] Portugal
• Vernacular Title: Dermatofibrosarcoma protuberans pigmentado (tumor de Bednar).
• PMID: 3068442 (Publication Type: Case Reports, English Abstract, Journal Article)

Topics

• Adult
• Child
• Female
• Fibrosarcoma (pathology, ultrastructure)
• Humans
• Male
• Skin Neoplasms (pathology, ultrastructure)