[Histiocytosis X. Review of the literature and a case report].

Abstract

Histiocytosis X is a non-lipid reticuloendotheliosis, characterized by histiocyte proliferation. The proliferating cells resemble the Langerhan's cells in the epidermis. The main clinical types include eosinophile granuloma, Hand-Schüller-Christian's disease (HSC) and Letterer-Siwe's disease (LS). Eosinophile granuloma is localized to the skeleton and runs a spontaneously benign course. HSC and LS are serious, generalized conditions. HSC runs a chronic and occasionally lethal course. LS usually runs a rapidly lethal course. LS commences before the age of three years while HSC occurs both in children and young adults. A case of HSC is described.

• Authors: B Hansen, P Schwarz
• Journal: Ugeskrift for laeger (Ugeskr Laeger) Vol. 151 Issue 1 Pg. 5-7 (Jan 02 1989) ISSN: 0041-5782 [Print] Denmark
• Vernacular Title: Histiocytosis X. Litteraturgennemgang og en sygehistorie.
• PMID: 2783500 (Publication Type: Case Reports, Journal Article)

Topics

• Adult
• Histiocytosis, Langerhans-Cell (diagnosis, diagnostic imaging, drug therapy)
• Humans
• Male
• Prognosis
• Radiography