Abstract |
PHACE syndrome is a disorder that features posterior fossa malformations, hemangiomas, arterial anomalies, coarctation of the aorta and cardiac defects, and eye abnormalities. PHACE syndrome includes abnormalities in several organ systems that may influence anesthetic management. We discuss the anesthetic management of a 26-year-old woman with PHACE syndrome presenting for cesarean delivery. Management included careful airway examination, slowly dosed epidural anesthesia, close hemodynamic monitoring aided by a radial arterial line, and continuous intraoperative neurologic assessment.
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Authors | Colleen Martel, Richard Robertson, Frank B Williams, R Clifton Moore, Allison Clark |
Journal | A & A case reports
(A A Case Rep)
Vol. 5
Issue 10
Pg. 176-8
(Nov 15 2015)
ISSN: 2325-7237 [Electronic] United States |
PMID | 26576049
(Publication Type: Case Reports, Journal Article)
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Topics |
- Abnormalities, Multiple
- Adult
- Anesthesia, Epidural
(methods)
- Anesthesia, Obstetrical
(methods)
- Aortic Coarctation
- Brain
(abnormalities)
- Cesarean Section
(methods)
- Cranial Fossa, Posterior
(abnormalities)
- Eye Abnormalities
- Female
- Hemangioma
- Humans
- Infant, Newborn
- Male
- Moyamoya Disease
(complications)
- Neurocutaneous Syndromes
- Neurologic Examination
- Pregnancy
- Pregnancy Outcome
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