Kidney transplantation in an adult patient with VACTERL association.

Abstract

The vertebral, anal, cardiac, tracheoesophageal, renal, and limb birth defects (VACTERL) association is a rare, non-random constellation of congenital abnormalities among which urinary tract anomalies can be included. In the presence of these anomalies, patients are suspected to have a higher rate of renal failure than average. We report a case of a 22-year-old woman with VACTERL association and consequent end stage renal failure. A live-related kidney transplant was carried out successfully and the postoperative course was uncomplicated. The patient had immediate graft function. Risk factors that may complicate kidney transplant surgery in this patient population as well as considerations relevant to peritransplant management are discussed.

• Authors: Sertac Cimen, Jordan Nantais, Sanem Guler, Joseph Lawen
• Journal: BMJ case reports (BMJ Case Rep) Vol. 2015 (Jun 23 2015) ISSN: 1757-790X [Electronic] England
• PMID: 26106170 (Publication Type: Case Reports, Journal Article)
• Copyright: 2015 BMJ Publishing Group Ltd.

Topics

• Adult
• Anal Canal (abnormalities)
• Esophagus (abnormalities)
• Female
• Follow-Up Studies
• Graft Survival
• Heart Defects, Congenital (complications)
• Humans
• Kidney (abnormalities)
• Kidney Failure, Chronic (surgery)
• Kidney Transplantation (methods)
• Limb Deformities, Congenital (complications)
• Recurrence
• Renal Insufficiency (surgery)
• Spine (abnormalities)
• Trachea (abnormalities)
• Treatment Outcome
• Urogenital Abnormalities (complications)