[Protein-losing enteropathy due to intestinal lymphangiectasis: a rare disease. Report of two cases].

Abstract

Congenital intestinal lymphangiectasis (LIP) is a protein-losing enteropathy that appears sporadically in children. It begins with edema due to hypoproteinemia and hypoalbuminemia, and in some cases with ascites, immunodeficience and hypocalcemic tetania. The purpose of this report is to present two patients with LIP which appeared during the first year of life. The diagnosis was certificated by upper gastrointestinal videoendoscopy and histological findings. Both patients were treated with a new formula containing mean chain triglycerides with an adequate response, not obtained before with a common semielemental formula.

• Authors: Horacio Sommaruga, Salomé Catalina Santarcángelo, Carlos Quintana, Daniel Navacchia
• Journal: Acta gastroenterologica Latinoamericana (Acta Gastroenterol Latinoam) Vol. 45 Issue 1 Pg. 70-5 (Mar 2015) ISSN: 0300-9033 [Print] Argentina
• Vernacular Title: Enteropatía perdedora de proteínas por linfangiectasia intestinal: una enfermedad rara. Presentación de 2 casos.
• PMID: 26076518 (Publication Type: Case Reports, English Abstract, Journal Article)

Topics

• Endoscopy, Gastrointestinal
• Female
• Humans
• Infant
• Lymphangiectasis, Intestinal (complications, diet therapy)
• Male
• Protein-Losing Enteropathies (diet therapy, etiology)
• Rare Diseases (diet therapy, etiology)