Turbinoplasty surgery for nasal obstruction in craniometaphyseal dysplasia: A case report and review of the literature.

Abstract

Craniometaphyseal dysplasia is a rare genetic condition characterised by hyperostosis of the skull base and sclerosis of craniofacial bones. This can cause nasal obstruction. This paper presents the case of a 14-year old with craniometaphyseal dysplasia presenting with nasal obstruction successfully treated with turbinoplasty. A literature search was conducted using PUBMED and EMBASE. In conclusion, in cases of craniometaphyseal dysplasia with nasal obstruction conventional techniques such as submucosal diathermy and outfracturing of inferior turbinates may not be adequate. Bony turbinoplasties along the whole length of the inferior turbinate may be required.

• Authors: V Twigg, S Carr, C Peres, S Mirza
• Journal: International journal of pediatric otorhinolaryngology (Int J Pediatr Otorhinolaryngol) Vol. 79 Issue 6 Pg. 935-937 (Jun 2015) ISSN: 1872-8464 [Electronic] Ireland
• PMID: 25890400 (Publication Type: Case Reports, Journal Article, Review)
• Copyright: Copyright © 2015 Elsevier Ireland Ltd. All rights reserved.

Topics

• Adolescent
• Bone Diseases, Developmental (complications, surgery)
• Craniofacial Abnormalities (complications, surgery)
• Humans
• Hyperostosis (complications, surgery)
• Hypertelorism (complications, surgery)
• Male
• Nasal Obstruction (etiology, surgery)
• Turbinates (surgery)