[Tracheobronchial prosthesis in Mounier-Kuhn syndrome: New perspectives].

Abstract

INTRODUCTION:

Mounier-Kuhn syndrome or tracheobronchomegaly is a rare congenital condition, the management of which is complex. We report the case of a patient who was treated with interventional endoscopy.

OBSERVATION:

We describe the case of a 74-year-old man with a diagnosis of tracheobronchomegaly who was admitted in 2003 with a background of deteriorating respiratory status and the occurrence of postural syncope. He initially received a tracheobronchial silicone Y prosthesis, extended with metal prostheses at the tracheal and bronchial level. This arrangement remained stable until 2011. He then began to develop episodes of asphyxia related to posterior dislocation of the tracheobronchial prosthesis, after breakage of the metallic mesh tracheal prosthesis. A new tracheobronchial prosthesis Y was then placed, custom-made from a 3D model of the airways. This was clinically and functionally effective.

DISCUSSION:

This case describes the management of a patient with Mounier-Kuhn syndrome by interventional bronchoscopy, with the adaptation of prosthetic materials, on an individual basis, to the anatomy of the patient's airway.

• Authors: M Sauvage, O Tiffet, J-M Vergnon
• Journal: Revue des maladies respiratoires (Rev Mal Respir) Vol. 32 Issue 5 Pg. 519-23 (May 2015) ISSN: 1776-2588 [Electronic] France
• Vernacular Title: Prothèse trachéobronchique dans le syndrome de Mounier-Kuhn : nouvelles perspectives.
• PMID: 25737189 (Publication Type: Case Reports, English Abstract, Journal Article)
• Copyright: Copyright © 2015 SPLF. Published by Elsevier Masson SAS. All rights reserved.

Chemical References

• Metals
• Silicones

Topics

• Aged
• Asphyxia (etiology)
• Bronchoscopy
• Continuous Positive Airway Pressure
• Humans
• Male
• Metals
• Precision Medicine
• Prostheses and Implants (adverse effects)
• Prosthesis Design
• Prosthesis Failure
• Prosthesis Implantation
• Silicones
• Sleep Apnea, Obstructive (etiology, therapy)
• Syncope (etiology)
• Tracheobronchomegaly (surgery)