Abstract | INTRODUCTION:
Mucopolysaccharidoses (MPSs) are a group of heredity storage diseases, transmitted in an autosomal recessive manner, associated with the accumulation of glycosaminoglycans (GAGs) in various tissues and organs. The concerned patients have multiple concomitant hereditary anomalies. Considering the craniofacial abnormality in these patients, airway management may be difficult for anesthesiologists. In these patients, preanesthetic assessment is necessary and performed with the accurate assessment of airways, consisting of the physical exam and radiography, MRI or CT of head and neck. An anesthesiologist should set up a "difficult intubation set" with a flexible fiber-optic bronchoscope and also, it may be necessary to discuss with an ear-nose and throat (ENT) specialist if required, for unpredicted emergency situations. CASE PRESENTATION: DISCUSSION:
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Authors | Mohsen Ziyaeifard, Rasoul Azarfarin, Rasoul Ferasatkish, Majid Dashti |
Journal | Research in cardiovascular medicine
(Res Cardiovasc Med)
Vol. 3
Issue 2
Pg. e17456
(May 2014)
ISSN: 2251-9572 [Print] India |
PMID | 25478534
(Publication Type: Case Reports)
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