Mounier-Kuhn Syndrome (MKS) is a rare congenital disease that presents with abnormal enlargement in the central airways. In MKS, tracheomegaly is accompanied by difficulty in expelling recurrent lung
infections and bronchiectasia. We presented a patient with MKS where commercially made
stents were inadequate for stabilization and a custom-made,
self-expandable metallic stent with a diameter of 28 mm and length of 100 mm was used.
Chest pain that was thought to develop due to the
stent and that disappeared after
stent removal may be considered the main complication leading to
stent removal.
Continuous positive airway pressure therapy (CPAP)
therapy was planned for the control of symptoms, which re-emerged after
stent removal. This case is presented as an example that complications developing due to the
stent as well as patient noncompliance may lead to
stent removal, even when useful results are obtained from treatment of MKS.