Review of accessory tragus with highlights of its associated syndromes.

Abstract

Accessory tragus is a developmental defect involving malformation of part of the external ear. It is a moderately rare congenital condition reported in 1858 by Birkett for the first time. Histological features of accessory tragus include a thin layer of stratum corneum with a rugated epidermis, presence of eccrine glands, and irregular spatial positioning of vellus hair follicles accompanied by sebaceous glands. Accessory tragus is commonly a limited deformity; however, it can be a sign of associated congenital syndromes. It has been shown to be associated with Goldenhar syndrome, Townes-Brocks syndrome, Treacher-Collins syndrome, VACTERL syndrome, and Wolf-Hirschhron syndrome. Surgical excision, the most common form of management of accessory tragus lesions, typically leads to a positive outcome. An extensive search was performed using pubmed.gov, Embase, MedLine, and Googlescholar.com using key words: accessory tragus, congenital malformations of ear, first branchial arch, and embryology. In this paper, we review the clinical and histological presentation, associated syndromes, management, and outcome of accessory tragus.

• Authors: Bahar Bahrani, Amor Khachemoune
• Journal: International journal of dermatology (Int J Dermatol) Vol. 53 Issue 12 Pg. 1442-6 (Dec 2014) ISSN: 1365-4632 [Electronic] England
• PMID: 25266223 (Publication Type: Journal Article, Review)
• Copyright: © 2014 The International Society of Dermatology.

Topics

• Abnormalities, Multiple
• Anal Canal (abnormalities)
• Anus, Imperforate
• Congenital Abnormalities (pathology, surgery)
• Ear Cartilage (abnormalities, surgery)
• Esophagus (abnormalities)
• Goldenhar Syndrome
• Hearing Loss, Sensorineural
• Heart Defects, Congenital
• Humans
• Kidney (abnormalities)
• Limb Deformities, Congenital
• Mandibulofacial Dysostosis
• Spine (abnormalities)
• Thumb (abnormalities)
• Trachea (abnormalities)
• Wolf-Hirschhorn Syndrome