Anesthesia for a child with Walker-Warburg syndrome.

Abstract

BACKGROUND AND OBJECTIVES:

Walker-Warburg Syndrome is a rare, autosomal recessive congenital muscular dystrophy manifested by central nervous system, eye malformations and possible multisystem involvement. The diagnosis is established by the presence of four criteria: congenital muscular dystrophy, type II lissencephaly, cerebellar malformation, and retinal malformation. Most of the syndromic children die in the first three years of life because of respiratory failure, pneumonia, seizures, hyperthermia and ventricular fibrillation.

CASE REPORT:

The anesthetic management of a two-months-old male child listed for elective ventriculo-peritoneal shunt operation was discussed.

CONCLUSIONS:

A careful anesthetic management is necessary due to the multisystem involvement. We reported anesthetic management of a two-months-old male child with Walker-Warburg Syndrome who was listed for elective ventriculo-peritoneal shunt operation.

• Authors: Emine Arzu Kose, Bulent Bakar, Gokay Ates, Didem Aliefendioglu, Alpaslan Apan
• Journal: Brazilian journal of anesthesiology (Elsevier) (Braz J Anesthesiol) 2014 Mar-Apr Vol. 64 Issue 2 Pg. 128-30 ISSN: 2352-2291 [Electronic] Brazil
• PMID: 24794457 (Publication Type: Case Reports, Journal Article)
• Copyright: Copyright © 2013 Sociedade Brasileira de Anestesiologia. Published by Elsevier Editora Ltda. All rights reserved.

Topics

• Anesthesia (methods)
• Humans
• Infant
• Male
• Walker-Warburg Syndrome (surgery)