Refsum's disease and cochlear implantation.

Abstract

OBJECTIVES:

The objective was to describe a case of bilateral cochlear implantation in a 59-year-old man with hearing and visual impairment due to Refsum's disease.

METHOD:

A retrospective case review was performed.

RESULTS:

After cochlear implantation, the patient demonstrated much improved audiometric performance and reported improved sound localization.

CONCLUSIONS:

Bilateral cochlear implantation is an important strategy in the improvement of hearing and quality of life in individuals with Refsum's disease.

• Authors: Claudia Nogueira, Thomasina Meehan, Gerard O'Donoghue
• Journal: The Annals of otology, rhinology, and laryngology (Ann Otol Rhinol Laryngol) Vol. 123 Issue 6 Pg. 425-7 (Jun 2014) ISSN: 0003-4894 [Print] United States
• PMID: 24690989 (Publication Type: Journal Article)

Topics

• Cochlear Implantation
• Hearing Loss, Bilateral (etiology, surgery)
• Hearing Loss, Sensorineural (etiology, surgery)
• Humans
• Male
• Middle Aged
• Refsum Disease (complications)
• Retrospective Studies
• Sound Localization
• Speech Perception