Anterior corpus callosotomy combined with anterior temporal resection with amygdalohippocampectomy: outcome in a patient with congenital bilateral perisylvian syndrome.
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| Abstract |
Congenital bilateral perisylvian syndrome (CBPS) is characterized by epilepsy, cognitive deficits, pseudobulbar palsy and diplegia of the facial, pharyngeal and masticatory muscles. Epilepsy has been described in nearly 90% of affected patients. The epilepsy is usually severe and pharmacoresistant in about 55 percent of CBPS patients. Until now, only 12 cases of surgical treatment on CBPS have been reported; the surgical treatment is usually corpus callosotomy. In this paper, we describe a previously unreported combination of anterior corpus callosotomy plus anterior temporal lobectomy with amygdalohippocampectomy for a patient with CBPS, resulting in a satisfactory clinical outcome. Based on this case, we suggest that palliative focal resective surgery combined with anterior corpus callosotomy should be considered when a predominance of the epileptiform discharges suggests focal onset in patients with CBPS. Meanwhile, the clinical decision to adopt this combination surgery must be based on a thorough pre-surgical evaluation, and should take into account the clinical, radiological, and EEG features.
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| Authors | Zhu Junming, Zhao Yuanyuan, Feng Fang, Fu Weiming, Hays Ryan, Zhang Jianmin, Feng Li, Jin Xiao, Chen Shuda |
| Journal | Turkish neurosurgery (Turk Neurosurg) Vol. 24 Issue 1 Pg. 70-4 ( 2014) ISSN: 2651-5032 [Electronic] Turkey |
| PMID | 24535795 (Publication Type: Case Reports, Journal Article) |
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