Thoracoscopic pericardiectomy for constrictive pericarditis in a pediatric patient with mulibrey nanism.

Abstract

Mulibrey nanism is a rare autosomal recessive disease with multisystem involvement. Clinical deterioration is most often related to cardiac involvement in the form of restrictive or constrictive disorders, and pericardiectomy may be required. We report a case of Mulibrey nanism in a patient of non-Finnish origin, where a thoracoscopic pericardiectomy helped in good palliation and clinical recovery.

• Authors: Georgi Christov, Michael Burch, Rachel Andrews, Jane Hurst, Michael Ashworth, Muhammad Mustafa, Nagarajan Muthialu
• Journal: World journal for pediatric & congenital heart surgery (World J Pediatr Congenit Heart Surg) Vol. 4 Issue 4 Pg. 442-3 (Oct 2013) ISSN: 2150-136X [Electronic] United States
• PMID: 24327644 (Publication Type: Case Reports, Journal Article)

Topics

• Child, Preschool
• Humans
• Male
• Mulibrey Nanism (complications)
• Pericardiectomy (methods)
• Pericarditis, Constrictive (etiology, surgery)