[An atypical form of neurosarcoidosis].

Abstract

INTRODUCTION:

Nervous system involvement occurs in 5 to 15% of the patients with sarcoidosis. Neurosarcoidosis remains very difficult to diagnose because clinical presentation and imaging characteristics lack specificity.

OBSERVATION:

We report a 26-year-old man who gradually developed headaches, memory disturbance and epilepsy. CT-scan and MRI showed a temporal-parietal cystic mass, secondary to a rare and focal form of hydrocephalus, called "trapped temporal horn" revealing neurosarcoidosis.

CONCLUSION:

The "entrapped temporal horn" is due to an obstacle on the cerebrospinal fluid pathway at the trigone of the lateral ventricle that seals off the temporal horn and the choroid plexus from the rest of the ventricular system. The obstacle is related to the granulomatous tissue of sarcoidosis. Therefore, the "trapped temporal horn" acts as a space occupying process, causing headaches, memory pain, hemiparesis, homonymous hemianopsia, and requires medico-surgical management.

• Authors: V Quenardelle, M Benmekhbi, J Aupy, C Dalvit, E Hirsch, A Benoilid
• Journal: La Revue de medecine interne (Rev Med Interne) Vol. 34 Issue 12 Pg. 776-9 (Dec 2013) ISSN: 1768-3122 [Electronic] France
• Vernacular Title: Neurosarcoïdose de présentation atypique.
• PMID: 24200098 (Publication Type: Case Reports, English Abstract, Journal Article)
• Copyright: Copyright © 2013 Société nationale française de médecine interne (SNFMI). Published by Elsevier SAS. All rights reserved.

Topics

• Adult
• Central Nervous System Diseases (diagnosis)
• Diagnosis, Differential
• Epilepsy (complications, diagnosis)
• Headache (complications, diagnosis)
• Humans
• Magnetic Resonance Imaging
• Male
• Memory Disorders (complications, diagnosis)
• Neuroimaging
• Sarcoidosis (diagnosis)