Abstract |
Primary hyperoxaluria type-1 (PH-1) is a rare autosomal recessive metabolic disorder leading to excessive oxalate production, deposition of calcium oxalate crystals in the kidney, nephrocalcinosis, progressive renal failure and systemic deposition of oxalate ( oxalosis). Combined liver and kidney transplantation (LKT), which has been accepted as the treatment of choice for PH-1, has considerably improved patient and graft survival. Herein, we report our experience of three children with PH-1 who underwent combined LKT, with a review of the literature.
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Authors | Prasad Nair, Torki Al-Otaibi, Narayanan Nampoory, Wafa'a Al-Qabandi, Tarek Said, Medhat Abdul Halim, Osama Gheith |
Journal | Saudi journal of kidney diseases and transplantation : an official publication of the Saudi Center for Organ Transplantation, Saudi Arabia
(Saudi J Kidney Dis Transpl)
Vol. 24
Issue 5
Pg. 969-75
(Sep 2013)
ISSN: 1319-2442 [Print] Saudi Arabia |
PMID | 24029263
(Publication Type: Case Reports, Journal Article, Review)
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Topics |
- Child
- Child, Preschool
- Consanguinity
- Female
- Graft Survival
- Humans
- Hyperoxaluria, Primary
(surgery)
- Kidney Transplantation
(methods)
- Liver Transplantation
(methods)
- Male
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