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Lehman syndrome: a new syndrome for pierre robin sequence.

Abstract
Lehman syndrome, or lateral meningocele syndrome, is characterized by facial dysmorphism, multiple lateral meningoceles, and skeletal abnormalities. Only nine cases have been described. We present a case of a 2-year-old boy presenting with micrognathia, glossoptosis, and hypertelorism as well as associated severe obstructive sleep apnea. He was submitted to bilateral mandibular distraction with external nonresorbable devices to correct Pierre Robin sequence (PRS). Later, multiple lateral meningoceles were identified, and a diagnosis of Lehman syndrome was made. Lehman syndrome must be considered in syndromic infants with PRS. Distraction osteogenesis is a safe procedure that is effective as a first choice in the treatment of patients with Lehman syndrome presenting with micrognathia.
AuthorsInês Correia-Sá, Ricardo Horta, Tiago Neto, José Amarante, Marisa Marques
JournalThe Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association (Cleft Palate Craniofac J) Vol. 52 Issue 3 Pg. 369-72 (05 2015) ISSN: 1545-1569 [Electronic] United States
PMID23962060 (Publication Type: Case Reports, Journal Article)
Topics
  • Abnormalities, Multiple (diagnostic imaging, surgery)
  • Humans
  • Infant
  • Magnetic Resonance Imaging
  • Male
  • Meningocele (diagnostic imaging, surgery)
  • Micrognathism (diagnostic imaging, surgery)
  • Osteogenesis, Distraction

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