Incidental (malignancy) and coincidental (idiopathic polydactylous longitudinal erythronychia) conditions in patients with segmental neurofibromatosis.

Abstract

Segmental neurofibromatosis (SNF) is an uncommon presentation of neurofibromatosis type 1 (NF-1). Although patients with SNF are at a lower risk for developing NF-l-associated complications, the estimated occurrence of related malignancies may be approaching the frequency observed in patients with NF-1. Idiopathic polydactylous longitudinal erythronychia also may be associated with SNF, though the frequency of this association remains to be determined.

• Authors: Philip R Cohen
• Journal: Cutis (Cutis) Vol. 91 Issue 4 Pg. 179-80 (Apr 2013) ISSN: 0011-4162 [Print] United States
• PMID: 23763076 (Publication Type: Journal Article)

Topics

• Adrenal Gland Neoplasms (epidemiology, etiology, pathology)
• Humans
• Nail Diseases (etiology, pathology)
• Neoplasms (epidemiology, etiology, pathology)
• Neurofibromatoses (complications, pathology)