Fertile eunuch syndrome in association with biventricular noncompaction, bicuspid aortic valve, severe aortic stenosis, and talipes equinovarus.

Abstract

Noncompaction of the ventricular myocardium is a congenital cardiomyopathy characterized by prominent ventricular trabeculations and deep intertrabecular recesses. In most cases, noncompaction is an isolated disease confined to the left ventricular myocardium. Fertile eunuch syndrome is a hypogonadotropic hormonal disorder in which the levels of testosterone and follicle-stimulating hormone are low. We report a case of biventricular noncompaction in association with bicuspid aortic valve and severe aortic stenosis in a 42-year-old man who was diagnosed with talipes equinovarus and fertile eunuch syndrome during childhood.

• Authors: Kazim Serhan Ozcan, Damirbek Osmonov, Servet Altay, Baris Gungor, Mehmet Eren
• Journal: Texas Heart Institute journal (Tex Heart Inst J) Vol. 40 Issue 2 Pg. 204-6 ( 2013) ISSN: 1526-6702 [Electronic] United States
• PMID: 23678225 (Publication Type: Case Reports, Journal Article)

Topics

• Adult
• Aortic Valve (abnormalities, surgery)
• Aortic Valve Stenosis (complications, diagnosis, surgery)
• Bicuspid Aortic Valve Disease
• Clubfoot (complications, diagnosis, surgery)
• Echocardiography, Doppler
• Eunuchism (complications, diagnosis, drug therapy)
• Heart Valve Diseases (complications, diagnosis, surgery)
• Heart Valve Prosthesis Implantation
• Heart Ventricles (abnormalities)
• Humans
• Male
• Severity of Illness Index
• Treatment Outcome