Total hip arthroplasty in a 17-year-old girl with progressive pseudorheumatoid dysplasia.

Abstract

Progressive pseudorheumatoid dysplasia is an autosomal recessively inherited skeletal disease. Progressive pseudorheumatoid dysplasia can involve multiple synovial joints, which then develop structural deformity and articular dysfunction. We report a case of progressive pseudorheumatoid dysplasia with polyarthropathy in a 17-year-old girl. Total hip arthroplasty was performed to treat persistent pain and stiffness by reconstructing a functional joint. Although we found arthroplasty to be an effective way of reconstructing a functional joint, treatment of the underlying cause is urgently required for this disease in the future.

• Authors: You-Shui Gao, Hao Ding, Chang-Qing Zhang
• Journal: Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseases (J Clin Rheumatol) Vol. 19 Issue 3 Pg. 138-41 (Apr 2013) ISSN: 1536-7355 [Electronic] United States
• PMID: 23519177 (Publication Type: Case Reports, Journal Article)

Topics

• Adolescent
• Arthropathy, Neurogenic (surgery)
• Arthroplasty, Replacement, Hip
• Female
• Hip Joint (surgery)
• Humans
• Joint Diseases (congenital)
• Treatment Outcome