Abstract | PURPOSE: To present a case of Haemangiopericytoma (HPC), a rare neopalsm which originates from the vascular pericytes. HPC occurs most commonly in adults. Only 5-10% of cases occur in children. Congenital orbital HPC is generally unknown in the field of ophthalmology. MATERIAL AND METHODS: A case of congenital, large exophthalmus is reported in a 1 day old male neonate. Imaging studies demonstrated a vascular, orbital mass involving skull base and cranial fossa. RESULTS: The diagnosis of HPC was established after histological exmination. Lesion did not qualify to surgical resection. The child was treated with chemotherapy for 10 months and a great regression of tumor was noted. There was no tumor recurrence during 4 years of a follow up. CONCLUSIONS:
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Authors | Barbara Chipczyńska, Mirosława Grałek |
Journal | Klinika oczna
(Klin Oczna)
Vol. 114
Issue 2
Pg. 124-6
( 2012)
ISSN: 0023-2157 [Print] Poland |
Vernacular Title | Guz oczodołu--haemangiopericytoma--u noworodka. |
PMID | 23346800
(Publication Type: Case Reports, Journal Article)
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Chemical References |
- Dactinomycin
- Vincristine
- Cyclophosphamide
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Topics |
- Antineoplastic Combined Chemotherapy Protocols
(therapeutic use)
- Child, Preschool
- Cranial Fossa, Posterior
(diagnostic imaging)
- Cyclophosphamide
(therapeutic use)
- Dactinomycin
(therapeutic use)
- Exophthalmos
(congenital)
- Follow-Up Studies
- Hemangiopericytoma
(congenital, diagnosis, drug therapy, pathology)
- Humans
- Infant
- Infant, Newborn
- Male
- Orbital Neoplasms
(congenital, diagnosis, drug therapy, pathology)
- Radiography
- Remission Induction
- Skull Base Neoplasms
(congenital, diagnosis, drug therapy, pathology)
- Vincristine
(therapeutic use)
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