Uterus didelphys with blind hemivagina and ipsilateral renal agenesis (Herlyn-Werner-Wunderlich syndrome) suspected on the presence of hydrocolpos on prenatal sonography.

Abstract

We report the case of a female neonate with ipsilateral renal agenesis and uterus didelphys with blind hemivagina, also known as Herlyn-Werner-Wunderlich (HWW) syndrome. Prenatal sonography revealed the absence of the left kidney and a retrovesical cystic lesion suspected as hydrometrocolpos. Postnatal evaluation confirmed that the cystic lesion was a hydrocolpos associated with double uterus and blind hemivagina (HWW syndrome). HWW syndrome can be suspected prenatally if a retrovesical cystic lesion is detected in a female fetus with unilateral absence of kidney.

• Authors: Byoung Hee Han, Sung Bin Park, Yu Jin Lee, Kyung Sang Lee, Yeon Kyung Lee
• Journal: Journal of clinical ultrasound : JCU (J Clin Ultrasound) Vol. 41 Issue 6 Pg. 380-2 ( 2013) ISSN: 1097-0096 [Electronic] United States
• PMID: 22678931 (Publication Type: Case Reports, Journal Article)
• Copyright: Copyright © 2012 Wiley Periodicals, Inc.

Topics

• Adult
• Female
• Humans
• Hydrocolpos (diagnostic imaging, etiology)
• Infant, Newborn
• Kidney (abnormalities, diagnostic imaging)
• Pregnancy
• Syndrome
• Ultrasonography, Prenatal
• Urogenital Abnormalities (complications, diagnostic imaging)
• Uterus (abnormalities, diagnostic imaging)
• Vagina (abnormalities, diagnostic imaging)