[Subsepsis allergica in a patient with type I polyglandular autoimmune syndrome].

Abstract

A 10.6 year old Turkish girl developed + the signs of a polyglandular autoimmune syndrome (PGA) type I since her first year of age. Apart from the endocrine and non-endocrine symptoms of PGA, she suffered from an acute state of illness with therapy-resistant fever and multiform exanthemas in the early course of disease. All included the criteria of Wissler-Fanconi syndrome became clear which has not yet been reported in association with PGA. Although this syndrome generally is considered an equivalent of Still's syndrome, rheumatoid symptoms could not be ascertained during the following 9-year-course of PGA.

• Authors: K H Spörkmann, R Eickhoff, H C Dominick
• Journal: Monatsschrift Kinderheilkunde : Organ der Deutschen Gesellschaft fur Kinderheilkunde (Monatsschr Kinderheilkd) Vol. 138 Issue 9 Pg. 619-22 (Sep 1990) ISSN: 0026-9298 [Print] Germany
• Vernacular Title: Subsepsis allergica bei einer Patientin mit polyglandulärem Autoimmunsyndrom Typ I.
• PMID: 2233764 (Publication Type: Case Reports, English Abstract, Journal Article)

Topics

• Addison Disease (diagnosis)
• Autoimmune Diseases (diagnosis)
• Candidiasis, Chronic Mucocutaneous (diagnosis)
• Child
• Consanguinity
• Diagnosis, Differential
• Female
• Humans
• Hypoparathyroidism (diagnosis)
• Hypothyroidism (diagnosis)
• Wissler's Syndrome (genetics)