Cardiac surgery in patients with acute intermittent porphyria.

Abstract

Acute intermittent porphyria (AIP) is a disorder of the heme biosynthesis pathway of a specific inherited enzymatic defect. Many different environmental factors such as drugs, calorie restriction, infection etc., often play a key role in triggering a porphiric acute attack. We describe a 50-year-old woman with AIP who underwent aortic valve replacement due to acute infective endocarditis and review the perioperative management of these patients.

• Authors: Filippo Benassi, Elena Righi, Paolo Cimato, Roberto Parravicini
• Journal: Journal of cardiac surgery (J Card Surg) Vol. 27 Issue 3 Pg. 331-4 (May 2012) ISSN: 1540-8191 [Electronic] United States
• PMID: 22176385 (Publication Type: Case Reports, Journal Article, Review)
• Copyright: © 2011 Wiley Periodicals, Inc.

Topics

• Aortic Valve Insufficiency (microbiology, surgery)
• Endocarditis, Bacterial (complications, diagnosis)
• Female
• Heart Valve Prosthesis Implantation
• Humans
• Middle Aged
• Porphyria, Acute Intermittent (complications)
• Staphylococcal Infections (complications, diagnosis)
• Staphylococcus hominis (isolation & purification)