Abstract |
Megalourethra is a rare spectrum of urologic malformations of penile corporal structures frequently associated with multiple congenital anomalies, such as prune belly syndrome or vertebral, anorectal, cardiac, trachea-esophageal, renal, and limb (VACTERL association) defects. A 6-year-old boy with VACTERL association and proximal urethral atresia with distal fusiform megalourethra underwent staged reconstruction, including appendicovesicostomy, perineal urethrostomy, and first-stage urethroplasty with a dorsal inlay free graft of megalourethra tissue to the proximal urethral atretic region, followed by second-stage urethroplasty. At 2.6 years of follow-up, he was continent, voids per urethra without postvoid residual urine volume, and no longer performs clean intermittent catheterization by way of the appendicovesicostomy.
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Authors | Aditya Bagrodia, Selcuk Yucel, Linda A Baker |
Journal | Urology
(Urology)
Vol. 78
Issue 6
Pg. 1417-9
(Dec 2011)
ISSN: 1527-9995 [Electronic] United States |
PMID | 21601242
(Publication Type: Case Reports, Journal Article)
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Copyright | Copyright © 2011 Elsevier Inc. All rights reserved. |
Topics |
- Abnormalities, Multiple
(surgery)
- Child
- Dilatation, Pathologic
(congenital)
- Humans
- Male
- Urethra
(abnormalities, surgery, transplantation)
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