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Deep anterior lamellar keratoplasty for Maroteaux-Lamy syndrome.

AbstractPURPOSE:
To present a case of Maroteaux-Lamy syndrome (MLS), which underwent deep anterior lamellar keratoplasty (DALK) for visual rehabilitation.
METHODS:
A 15-year-old girl with MLS was admitted with severe corneal opacity. We performed DALK on her left eye for visual rehabilitation. Big-bubble technique was used to perform lamellar separation.
RESULTS:
Corneal graft was clear 24 months after surgery. Best spectacle-corrected visual acuity of left eye was 20/25 with the correction of +0.75/-0.50 diopters × 170. At the last follow-up, in vivo confocal microscopy revealed mild haze in the posterior stroma at the graft interface level. Endothelial cell count was 2473.4 cells per square millimeter using a noncontact specular microscope.
CONCLUSIONS:
Given systemic problems in patients with MLS and less postoperative complications of DALK in comparison with penetrating keratoplasty, it seems DALK is the better choice for these patients.
AuthorsMohsen Rahmati-Kamel, Mohammadali Javadi, Ahmad Shojaei, Medi Eslani, Farid Karimian
JournalCornea (Cornea) Vol. 29 Issue 12 Pg. 1459-61 (Dec 2010) ISSN: 1536-4798 [Electronic] United States
PMID20856106 (Publication Type: Case Reports, Journal Article)
Topics
  • Adolescent
  • Cell Count
  • Corneal Diseases (pathology, surgery)
  • Corneal Transplantation
  • Endothelium, Corneal (pathology)
  • Female
  • Humans
  • Mucopolysaccharidosis VI (pathology, surgery)
  • Vision Disorders (rehabilitation)
  • Visual Acuity (physiology)

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