Congenital erythropoietic porphyria: anesthetic implications.

Abstract

Congenital erythropoietic porphyria is a rare error of heme metabolism. Derangement of heme metabolism leads to disfiguration, phototoxicity, and the precipitation of porphyric crises. This case report discusses the myriad perioperative considerations in a patient with congenital erythropoietic porphyria.

• Authors: Mritunjay Kumar, Somnath Bose, Vanlal Darlong, Jyotsna Punj
• Journal: Journal of anesthesia (J Anesth) Vol. 23 Issue 4 Pg. 569-71 ( 2009) ISSN: 1438-8359 [Electronic] Japan
• PMID: 19921367 (Publication Type: Case Reports, Journal Article)

Chemical References

• Heme

Topics

• Adult
• Anesthesia, General
• Blindness (etiology, surgery)
• Dermatitis, Phototoxic (etiology)
• Endophthalmitis (surgery)
• Hand Deformities, Acquired (complications)
• Heme (metabolism)
• Humans
• Male
• Ophthalmologic Surgical Procedures
• Pain, Postoperative (drug therapy)
• Perioperative Care
• Porphyria, Erythropoietic (complications, pathology)
• Postoperative Complications (etiology, therapy)