Juvenile linear scleroderma with unique forms of renal involvement.

Abstract

Linear scleroderma is the most common type of juvenile localized scleroderma, which usually involves the limbs. The linear lesions may extend through the dermis, subcutaneous tissue, muscles, and the underlying bone, leading to significant functional and cosmetic deformities. Renal involvement in juvenile localized scleroderma is a rare manifestation. Here we report two cases with juvenile linear scleroderma and unique renal manifestations, including unilateral renal arterial stenosis and immunoglobulin M nephropathy.

• Authors: Belde Kasap, Alper Soylu, Mehmet Türkmen, Yiğit Göktay, Sülen Sarioğlu, Can Oztürk, Ozgür Kasapçopur, Salih Kavukcu
• Journal: Pediatric nephrology (Berlin, Germany) (Pediatr Nephrol) Vol. 24 Issue 10 Pg. 2041-5 (Oct 2009) ISSN: 1432-198X [Electronic] Germany
• PMID: 19475430 (Publication Type: Case Reports, Journal Article)

Chemical References

• Immunoglobulin M

Topics

• Child
• Child, Preschool
• Female
• Humans
• Immunoglobulin M
• Infant
• Kidney Diseases (etiology, pathology, physiopathology)
• Leg Length Inequality (etiology, pathology)
• Renal Artery Obstruction (etiology, pathology)
• Scleroderma, Localized (complications, pathology, physiopathology)