Phacomatosis pigmentopigmentalis: aberrant Mongolian spots and segmental café au lait macules.

Abstract

We report a case of an otherwise healthy male newborn, with segmental café au lait spots on his left buttocks and left thigh down to the medial knee, in a nevoid pattern, and an aberrant Mongolian spot on the ipsilateral cheek of the buttocks in a checkerboard pattern. We propose the name phacomatosis pigmentopigmentalis in analogy to phacomatosis pigmentovascularis, and phacomatosis pigmentokeratotica.

• Authors: Ronni Wolf, Danny Wolf, Batya Davidovici
• Journal: Pediatric dermatology (Pediatr Dermatol) Vol. 26 Issue 2 Pg. 228-9 ( 2009) ISSN: 1525-1470 [Electronic] United States
• PMID: 19419484 (Publication Type: Case Reports, Journal Article)

Topics

• Cafe-au-Lait Spots (complications, pathology)
• Humans
• Infant, Newborn
• Male
• Mongolian Spot (complications, pathology)