Long segment congenital tracheal stenosis in twins successfully treated by slide tracheoplasty.

Abstract

Long segment congenital tracheal stenosis (LSCTS), associated with complete tracheal rings, is a rare condition, difficult to manage and historically associated with high mortality rate. We report two pairs of identical twins all affected by LSCTS successfully treated by sliding tracheoplasty. All had severe respiratory distress. Three infants had left pulmonary artery (LPA) sling and one intra-cardiac malformation. Slide tracheoplasty was done under cardiopulmonary bypass, and cardiovascular malformations were corrected at the same time. One child needed plication of paralyzed right hemi-diaphragm and another distal tracheal Palmaz stent insertion due severe tracheobronchomalacia. All children are doing well during 6 months follow-up. Slide tracheoplasty seems to produce the same good early results in twins as for singletons with LSCTS.

• Authors: Jose Carlos Fraga, Haney O S Gabra, Emmeline E Calkoen, Clare A McLaren, Derek J Roebuck, Martin J Elliott
• Journal: Journal of pediatric surgery (J Pediatr Surg) Vol. 44 Issue 3 Pg. 640-3 (Mar 2009) ISSN: 1531-5037 [Electronic] United States
• PMID: 19302875 (Publication Type: Journal Article)

Topics

• Abnormalities, Multiple
• Bronchoscopy
• Cleft Palate (epidemiology)
• Diseases in Twins (surgery)
• Female
• Heart Septal Defects, Atrial (epidemiology, surgery)
• Humans
• Infant, Newborn
• Pulmonary Artery (surgery)
• Trachea (surgery)
• Tracheal Stenosis (surgery)
• Twins, Monozygotic