Papillon-Lefevre syndrome: a case report.

Abstract

Papillon-Lefevre syndrome is a rare autosomal recessive genetic disorder. The clinical manifestations include palmer planter hyperkeratosis with precocious progressive periodontal disease that results in premature exfoliation of primary and permanent dentitions. Patients are often edentulous at an early age. This is a case report of prosthodontic rehabilitation of a 15-year-old girl with Papillon-Lefevre syndrome.

• Authors: P Subramaniam, S Mathew, K K Gupta
• Journal: Journal of the Indian Society of Pedodontics and Preventive Dentistry (J Indian Soc Pedod Prev Dent) Vol. 26 Issue 4 Pg. 171-4 (Dec 2008) ISSN: 0970-4388 [Print] India
• PMID: 19008627 (Publication Type: Case Reports, Journal Article)

Topics

• Adolescent
• Alveolar Bone Loss (physiopathology)
• Denture, Complete
• Female
• Follow-Up Studies
• Humans
• Mouth, Edentulous (rehabilitation)
• Papillon-Lefevre Disease (physiopathology)
• Periodontitis (physiopathology)
• Tooth Loss (rehabilitation)